Codify By AAPC
ICD 10 Range Certain disorders involving the immune mechanism
1
Immunodeficiency with predominantly antibody defects( D80 )
2
Hereditary hypogammaglobulinemia( D80.0 )
3
Nonfamilial hypogammaglobulinemia( D80.1 )
4
Selective deficiency of immunoglobulin A [IgA]( D80.2 )
5
Selective deficiency of immunoglobulin G [IgG] subclasses( D80.3 )
6
Selective deficiency of immunoglobulin M [IgM]( D80.4 )
7
Immunodeficiency with increased immunoglobulin M [IgM]( D80.5 )
8
Antibody deficiency with near-normal immunoglobulins or with hyperimmunoglobulinemia( D80.6 )
9
Transient hypogammaglobulinemia of infancy( D80.7 )
10
Other immunodeficiencies with predominantly antibody defects( D80.8 )
11
Immunodeficiency with predominantly antibody defects, unspecified( D80.9 )
12
Combined immunodeficiencies( D81 )
13
Severe combined immunodeficiency [SCID] with reticular dysgenesis( D81.0 )
14
Severe combined immunodeficiency [SCID] with low T- and B-cell numbers( D81.1 )
15
Severe combined immunodeficiency [SCID] with low or normal B-cell numbers( D81.2 )
16
Adenosine deaminase [ADA] deficiency( D81.3 )
17
Adenosine deaminase deficiency, unspecified( D81.30 )
18
Severe combined immunodeficiency due to adenosine deaminase deficiency( D81.31 )
19
Adenosine deaminase 2 deficiency( D81.32 )
20
Other adenosine deaminase deficiency( D81.39 )
21
Nezelof's syndrome( D81.4 )
22
Purine nucleoside phosphorylase [PNP] deficiency( D81.5 )
23
Major histocompatibility complex class I deficiency( D81.6 )
24
Major histocompatibility complex class II deficiency( D81.7 )
25
Other combined immunodeficiencies( D81.8 )
26
Biotin-dependent carboxylase deficiency( D81.81 )
27
Biotinidase deficiency( D81.810 )
28
Other biotin-dependent carboxylase deficiency( D81.818 )
29
Biotin-dependent carboxylase deficiency, unspecified( D81.819 )
30
Activated Phosphoinositide 3-kinase Delta Syndrome [APDS]( D81.82 )
31
Other combined immunodeficiencies( D81.89 )
32
Combined immunodeficiency, unspecified( D81.9 )
33
Immunodeficiency associated with other major defects( D82 )
34
Wiskott-Aldrich syndrome( D82.0 )
35
Di George's syndrome( D82.1 )
36
Immunodeficiency with short-limbed stature( D82.2 )
37
Immunodeficiency following hereditary defective response to Epstein-Barr virus( D82.3 )
38
Hyperimmunoglobulin E [IgE] syndrome( D82.4 )
39
Immunodeficiency associated with other specified major defects( D82.8 )
40
Immunodeficiency associated with major defect, unspecified( D82.9 )
41
Common variable immunodeficiency( D83 )
42
Common variable immunodeficiency with predominant abnormalities of B-cell numbers and function( D83.0 )
43
Common variable immunodeficiency with predominant immunoregulatory T-cell disorders( D83.1 )
44
Common variable immunodeficiency with autoantibodies to B- or T-cells( D83.2 )
45
Other common variable immunodeficiencies( D83.8 )
46
Common variable immunodeficiency, unspecified( D83.9 )
47
Other immunodeficiencies( D84 )
48
Lymphocyte function antigen-1 [LFA-1] defect( D84.0 )
49
Defects in the complement system( D84.1 )
50
Other specified immunodeficiencies( D84.8 )
51
Immunodeficiency due to conditions classified elsewhere( D84.81 )
52
Immunodeficiency due to drugs and external causes( D84.82 )
53
Immunodeficiency due to drugs( D84.821 )
54
Immunodeficiency due to external causes( D84.822 )
55
Other immunodeficiencies( D84.89 )
56
Immunodeficiency, unspecified( D84.9 )
57
Sarcoidosis( D86 )
58
Sarcoidosis of lung( D86.0 )
59
Sarcoidosis of lymph nodes( D86.1 )
60
Sarcoidosis of lung with sarcoidosis of lymph nodes( D86.2 )
61
Sarcoidosis of skin( D86.3 )
62
Sarcoidosis of other sites( D86.8 )
63
Sarcoid meningitis( D86.81 )
64
Multiple cranial nerve palsies in sarcoidosis( D86.82 )
65
Sarcoid iridocyclitis( D86.83 )
66
Sarcoid pyelonephritis( D86.84 )
67
Sarcoid myocarditis( D86.85 )
68
Sarcoid arthropathy( D86.86 )
69
Sarcoid myositis( D86.87 )
70
Sarcoidosis of other sites( D86.89 )
71
Sarcoidosis, unspecified( D86.9 )
72
Other disorders involving the immune mechanism, not elsewhere classified( D89 )
73
Polyclonal hypergammaglobulinemia( D89.0 )
74
Cryoglobulinemia( D89.1 )
75
Hypergammaglobulinemia, unspecified( D89.2 )
76
Immune reconstitution syndrome( D89.3 )
77
Mast cell activation syndrome and related disorders( D89.4 )
78
Mast cell activation, unspecified( D89.40 )
79
Monoclonal mast cell activation syndrome( D89.41 )
80
Idiopathic mast cell activation syndrome( D89.42 )
81
Secondary mast cell activation( D89.43 )
82
Hereditary alpha tryptasemia( D89.44 )
83
Other mast cell activation disorder( D89.49 )
84
Other specified disorders involving the immune mechanism, not elsewhere classified( D89.8 )
85
Graft-versus-host disease( D89.81 )
86
Acute graft-versus-host disease( D89.810 )
87
Chronic graft-versus-host disease( D89.811 )
88
Acute on chronic graft-versus-host disease( D89.812 )
89
Graft-versus-host disease, unspecified( D89.813 )
90
Autoimmune lymphoproliferative syndrome [ALPS]( D89.82 )
91
Cytokine release syndrome( D89.83 )
92
Cytokine release syndrome, grade 1( D89.831 )
93
Cytokine release syndrome, grade 2( D89.832 )
94
Cytokine release syndrome, grade 3( D89.833 )
95
Cytokine release syndrome, grade 4( D89.834 )
96
Cytokine release syndrome, grade 5( D89.835 )
97
Cytokine release syndrome, grade unspecified( D89.839 )
98
IgG4-related disease( D89.84 )
99
Other specified disorders involving the immune mechanism, not elsewhere classified( D89.89 )
100
Disorder involving the immune mechanism, unspecified( D89.9 )