ICD 10 Range Other congenital malformations

• 1 Congenital ichthyosis( Q80 )

• 2 Ichthyosis vulgaris( Q80.0 )

• 3 X-linked ichthyosis( Q80.1 )

• 4 Lamellar ichthyosis( Q80.2 )

• 5 Congenital bullous ichthyosiform erythroderma( Q80.3 )

• 6 Harlequin fetus( Q80.4 )

• 7 Other congenital ichthyosis( Q80.8 )

• 8 Congenital ichthyosis, unspecified( Q80.9 )

• 9 Epidermolysis bullosa( Q81 )

• 10 Epidermolysis bullosa simplex( Q81.0 )

• 11 Epidermolysis bullosa letalis( Q81.1 )

• 12 Epidermolysis bullosa dystrophica( Q81.2 )

• 13 Other epidermolysis bullosa( Q81.8 )

• 14 Epidermolysis bullosa, unspecified( Q81.9 )

• 15 Other congenital malformations of skin( Q82 )

• 16 Hereditary lymphedema( Q82.0 )

• 17 Xeroderma pigmentosum( Q82.1 )

• 18 Congenital cutaneous mastocytosis( Q82.2 )

• 19 Incontinentia pigmenti( Q82.3 )

• 20 Ectodermal dysplasia (anhidrotic)( Q82.4 )

• 21 Congenital non-neoplastic nevus( Q82.5 )

• 22 Congenital sacral dimple( Q82.6 )

• 23 Other specified congenital malformations of skin( Q82.8 )

• 24 Congenital malformation of skin, unspecified( Q82.9 )

• 25 Congenital malformations of breast( Q83 )

• 26 Congenital absence of breast with absent nipple( Q83.0 )

• 27 Accessory breast( Q83.1 )

• 28 Absent nipple( Q83.2 )

• 29 Accessory nipple( Q83.3 )

• 30 Other congenital malformations of breast( Q83.8 )

• 31 Congenital malformation of breast, unspecified( Q83.9 )

• 32 Other congenital malformations of integument( Q84 )

• 33 Congenital alopecia( Q84.0 )

• 34 Congenital morphological disturbances of hair, not elsewhere classified( Q84.1 )

• 35 Other congenital malformations of hair( Q84.2 )

• 36 Anonychia( Q84.3 )

• 37 Congenital leukonychia( Q84.4 )

• 38 Enlarged and hypertrophic nails( Q84.5 )

• 39 Other congenital malformations of nails( Q84.6 )

• 40 Other specified congenital malformations of integument( Q84.8 )

• 41 Congenital malformation of integument, unspecified( Q84.9 )

• 42 Phakomatoses, not elsewhere classified( Q85 )

• 43 Neurofibromatosis (nonmalignant)( Q85.0 )

• 44 Neurofibromatosis, unspecified( Q85.00 )

• 45 Neurofibromatosis, type 1( Q85.01 )

• 46 Neurofibromatosis, type 2( Q85.02 )

• 47 Schwannomatosis( Q85.03 )

• 48 Other neurofibromatosis( Q85.09 )

• 49 Tuberous sclerosis( Q85.1 )

• 50 Other phakomatoses, not elsewhere classified( Q85.8 )

• 51 PTEN hamartoma tumor syndrome( Q85.81 )

• 52 Other Cowden syndrome( Q85.82 )

• 53 Von Hippel-Lindau syndrome( Q85.83 )

• 54 Other phakomatoses, not elsewhere classified( Q85.89 )

• 55 Phakomatosis, unspecified( Q85.9 )

• 56 Congenital malformation syndromes due to known exogenous causes, not elsewhere classified( Q86 )

• 57 Fetal alcohol syndrome (dysmorphic)( Q86.0 )

• 58 Fetal hydantoin syndrome( Q86.1 )

• 59 Dysmorphism due to warfarin( Q86.2 )

• 60 Other congenital malformation syndromes due to known exogenous causes( Q86.8 )

• 61 Other specified congenital malformation syndromes affecting multiple systems( Q87 )

• 62 Congenital malformation syndromes predominantly affecting facial appearance( Q87.0 )

• 63 Congenital malformation syndromes predominantly associated with short stature( Q87.1 )

• 64 Prader-Willi syndrome( Q87.11 )

• 65 Other congenital malformation syndromes predominantly associated with short stature( Q87.19 )

• 66 Congenital malformation syndromes predominantly involving limbs( Q87.2 )

• 67 Congenital malformation syndromes involving early overgrowth( Q87.3 )

• 68 Marfan syndrome( Q87.4 )

• 69 Marfan syndrome, unspecified( Q87.40 )

• 70 Marfan syndrome with cardiovascular manifestations( Q87.41 )

• 71 Marfan syndrome with aortic dilation( Q87.410 )

• 72 Marfan syndrome with other cardiovascular manifestations( Q87.418 )

• 73 Marfan syndrome with ocular manifestations( Q87.42 )

• 74 Marfan syndrome with skeletal manifestation( Q87.43 )

• 75 Other congenital malformation syndromes with other skeletal changes( Q87.5 )

• 76 Other specified congenital malformation syndromes, not elsewhere classified( Q87.8 )

• 77 Alport syndrome( Q87.81 )

• 78 Arterial tortuosity syndrome( Q87.82 )

• 79 Bardet-Biedl syndrome( Q87.83 )

• 80 Laurence-Moon syndrome( Q87.84 )

• 81 MED13L syndrome( Q87.85 )

• 82 Other specified congenital malformation syndromes, not elsewhere classified( Q87.89 )

• 83 Other congenital malformations, not elsewhere classified( Q89 )

• 84 Congenital absence and malformations of spleen( Q89.0 )

• 85 Asplenia (congenital)( Q89.01 )

• 86 Congenital malformations of spleen( Q89.09 )

• 87 Congenital malformations of adrenal gland( Q89.1 )

• 88 Congenital malformations of other endocrine glands( Q89.2 )

• 89 Situs inversus( Q89.3 )

• 90 Conjoined twins( Q89.4 )

• 91 Multiple congenital malformations, not elsewhere classified( Q89.7 )

• 92 Other specified congenital malformations( Q89.8 )

• 93 Congenital malformation, unspecified( Q89.9 )