ICD 10 Range Systemic connective tissue disorders

• 1 Polyarteritis nodosa and related conditions( M30 )

• 2 Polyarteritis nodosa( M30.0 )

• 3 Polyarteritis with lung involvement [Churg-Strauss]( M30.1 )

• 4 Juvenile polyarteritis( M30.2 )

• 5 Mucocutaneous lymph node syndrome [Kawasaki]( M30.3 )

• 6 Other conditions related to polyarteritis nodosa( M30.8 )

• 7 Other necrotizing vasculopathies( M31 )

• 8 Hypersensitivity angiitis( M31.0 )

• 9 Thrombotic microangiopathy( M31.1 )

• 10 Thrombotic microangiopathy, unspecified( M31.10 )

• 11 Hematopoietic stem cell transplantation-associated thrombotic microangiopathy [HSCT-TMA]( M31.11 )

• 12 Other thrombotic microangiopathy( M31.19 )

• 13 Lethal midline granuloma( M31.2 )

• 14 Wegener's granulomatosis( M31.3 )

• 15 Wegener's granulomatosis without renal involvement( M31.30 )

• 16 Wegener's granulomatosis with renal involvement( M31.31 )

• 17 Aortic arch syndrome [Takayasu]( M31.4 )

• 18 Giant cell arteritis with polymyalgia rheumatica( M31.5 )

• 19 Other giant cell arteritis( M31.6 )

• 20 Microscopic polyangiitis( M31.7 )

• 21 Other specified necrotizing vasculopathies( M31.8 )

• 22 Necrotizing vasculopathy, unspecified( M31.9 )

• 23 Systemic lupus erythematosus (SLE)( M32 )

• 24 Drug-induced systemic lupus erythematosus( M32.0 )

• 25 Systemic lupus erythematosus with organ or system involvement( M32.1 )

• 26 Systemic lupus erythematosus, organ or system involvement unspecified( M32.10 )

• 27 Endocarditis in systemic lupus erythematosus( M32.11 )

• 28 Pericarditis in systemic lupus erythematosus( M32.12 )

• 29 Lung involvement in systemic lupus erythematosus( M32.13 )

• 30 Glomerular disease in systemic lupus erythematosus( M32.14 )

• 31 Tubulo-interstitial nephropathy in systemic lupus erythematosus( M32.15 )

• 32 Other organ or system involvement in systemic lupus erythematosus( M32.19 )

• 33 Other forms of systemic lupus erythematosus( M32.8 )

• 34 Systemic lupus erythematosus, unspecified( M32.9 )

• 35 Dermatopolymyositis( M33 )

• 36 Juvenile dermatomyositis( M33.0 )

• 37 Juvenile dermatomyositis, organ involvement unspecified( M33.00 )

• 38 Juvenile dermatomyositis with respiratory involvement( M33.01 )

• 39 Juvenile dermatomyositis with myopathy( M33.02 )

• 40 Juvenile dermatomyositis without myopathy( M33.03 )

• 41 Juvenile dermatomyositis with other organ involvement( M33.09 )

• 42 Other dermatomyositis( M33.1 )

• 43 Other dermatomyositis, organ involvement unspecified( M33.10 )

• 44 Other dermatomyositis with respiratory involvement( M33.11 )

• 45 Other dermatomyositis with myopathy( M33.12 )

• 46 Other dermatomyositis without myopathy( M33.13 )

• 47 Other dermatomyositis with other organ involvement( M33.19 )

• 48 Polymyositis( M33.2 )

• 49 Polymyositis, organ involvement unspecified( M33.20 )

• 50 Polymyositis with respiratory involvement( M33.21 )

• 51 Polymyositis with myopathy( M33.22 )

• 52 Polymyositis with other organ involvement( M33.29 )

• 53 Dermatopolymyositis, unspecified( M33.9 )

• 54 Dermatopolymyositis, unspecified, organ involvement unspecified( M33.90 )

• 55 Dermatopolymyositis, unspecified with respiratory involvement( M33.91 )

• 56 Dermatopolymyositis, unspecified with myopathy( M33.92 )

• 57 Dermatopolymyositis, unspecified without myopathy( M33.93 )

• 58 Dermatopolymyositis, unspecified with other organ involvement( M33.99 )

• 59 Systemic sclerosis [scleroderma]( M34 )

• 60 Progressive systemic sclerosis( M34.0 )

• 61 CR(E)ST syndrome( M34.1 )

• 62 Systemic sclerosis induced by drug and chemical( M34.2 )

• 63 Other forms of systemic sclerosis( M34.8 )

• 64 Systemic sclerosis with lung involvement( M34.81 )

• 65 Systemic sclerosis with myopathy( M34.82 )

• 66 Systemic sclerosis with polyneuropathy( M34.83 )

• 67 Other systemic sclerosis( M34.89 )

• 68 Systemic sclerosis, unspecified( M34.9 )

• 69 Other systemic involvement of connective tissue( M35 )

• 70 Sjogren syndrome( M35.0 )

• 71 Sjogren syndrome, unspecified( M35.00 )

• 72 Sjogren syndrome with keratoconjunctivitis( M35.01 )

• 73 Sjogren syndrome with lung involvement( M35.02 )

• 74 Sjogren syndrome with myopathy( M35.03 )

• 75 Sjogren syndrome with tubulo-interstitial nephropathy( M35.04 )

• 76 Sjogren syndrome with inflammatory arthritis( M35.05 )

• 77 Sjogren syndrome with peripheral nervous system involvement( M35.06 )

• 78 Sjogren syndrome with central nervous system involvement( M35.07 )

• 79 Sjogren syndrome with gastrointestinal involvement( M35.08 )

• 80 Sjogren syndrome with glomerular disease( M35.0A )

• 81 Sjogren syndrome with vasculitis( M35.0B )

• 82 Sjogren syndrome with dental involvement( M35.0C )

• 83 Sjogren syndrome with other organ involvement( M35.09 )

• 84 Other overlap syndromes( M35.1 )

• 85 Behcet's disease( M35.2 )

• 86 Polymyalgia rheumatica( M35.3 )

• 87 Diffuse (eosinophilic) fasciitis( M35.4 )

• 88 Multifocal fibrosclerosis( M35.5 )

• 89 Relapsing panniculitis [Weber-Christian]( M35.6 )

• 90 Hypermobility syndrome( M35.7 )

• 91 Other specified systemic involvement of connective tissue( M35.8 )

• 92 Multisystem inflammatory syndrome( M35.81 )

• 93 Other specified systemic involvement of connective tissue( M35.89 )

• 94 Systemic involvement of connective tissue, unspecified( M35.9 )

• 95 Systemic disorders of connective tissue in diseases classified elsewhere( M36 )

• 96 Dermato(poly)myositis in neoplastic disease( M36.0 )

• 97 Arthropathy in neoplastic disease( M36.1 )

• 98 Hemophilic arthropathy( M36.2 )

• 99 Arthropathy in other blood disorders( M36.3 )

• 100 Arthropathy in hypersensitivity reactions classified elsewhere( M36.4 )

• 101 Systemic disorders of connective tissue in other diseases classified elsewhere( M36.8 )