Neurology & Pain Management Coding Alert

Question: How do we report Lhermitte-Duclos in ICD-9?

Alaska Subscriber

Answer: You may report code 215.0 (Other benign neoplasm of connective and other soft tissue of head face and neck) for this condition.

Explanation: Lhermitte-Duclos disease (LDD) is a dysplastic gangliocytoma of the cerebellum. It is essentially a slow growing benign tumor of the cerebellum. There is a diffuse hypertrophy of the stratum granulosum of the cerebellum. LDD is characterized by abnormal development and enlargement of the cerebellum, and increased intracranial pressure. Symptoms may include headache, nausea, cerebellar dysfunction, hydrocephalus, ataxia (problems with movement and coordination), and visual disturbances.