Question: What is the difference between hypertension and pulmonary hypertension? What is the correct way to code pulmonary HTN? Montana Subscriber Answer: Systemic hypertension (HTN) and pulmonary hypertension (PH) sound similar — and to a certain extent, they are. The word “hypertension” in both names means that pressure is high in the arteries, and the heart is working overtime to pump blood into them. The distinction? Where in the vasculature this high pressure exists. With systemic HTN, pressure is high in arteries throughout the body, whereas, in PH, there is high blood pressure in the pulmonary arteries, which carry oxygen-poor blood from the heart to the lungs.
When your provider diagnoses a patient with PH, report the category I27.- (Other pulmonary heart diseases) code that best aligns with the documentation: Tip: “For secondary pulmonary hypertension (I27.1, I27.2-), code also any associated conditions or adverse effects of drugs or toxins. The sequencing is based on the reason for the encounter, except for adverse effects of drugs,” per the ICD-10-CM guidelines.